A pheochromocytoma is a neuroendocrine tumor arising from the adrenal glands that produces high amounts of catecholamines that include metanephrine, normetanephrine, epinephrine, orepinephrine and dopamine as well as their metabolites.  Patients who are diagnosed with pheochromocytomas typically show excessive amounts of these hormones / metabolites but that is not always the case and they may be found on radio graphic screening for other conditions or incidentally at the time of a surgical procedure. Fewer than 20% of these tumors are metastatic (this number is much higher in those patients with a SDHB gene mutation) and a surgical resection or removal of the pheochromocytoma is the recommended treatment. Surgery should only be performed at centers experienced in the management of this rare disorder.